Fibrosarcoma, [s8]uncommon

Fibrosarcomas usually arise from the muscle sheath or periosteum of the thigh, lower leg, or back. The patient, who is usually between between 30 and 50, presents with a firm to hard mass which is usually painless in its early stages. Fibrosarcomas are moderately malignant, and spread by local infiltration. Lymphatic and blood-borne spread to the lung are unusual.

FIBROSARCOMA DIFFERENTIAL DIAGNOSIS and STAGING are the same as for a rhabdomyosarcoma (32.9). 30% to 40% of treated cases survive 5 years.

TREATMENT. Do a wide local excision. Consider amputation if you cannot remove a limb tumour efficiently. Response is only temporary, so chemotherapy is of little value.